Overview of Pompe Disease
Treating Pompe
Current Research
Supportive TherapiesPhysical Therapy
Patients who begin to lose mobility due to weakened muscles may also benefit from physical therapy. A customized exercise and/or physical therapy program developed by a health care professional may help to preserve range of motion and strength, while the use of assistive devices such as orthotics, canes, or walkers may help with ambulation. In advanced cases, a wheelchair may be indicated.
For young children with muscle weakness, physical therapy may:
- Help them learn how to move and interact with their environment
- Help to prevent contractures
- Provide ways for parents, with instruction from a physical therapist, to facilitate a young child's growth and development
- Preserve range of motion and strength, as well as minimizing discomfort from musculoskeletal changes as Pompe disease progresses
Some physicians have prescribed exercise programs that may help patients with late-onset Pompe disease stay conditioned and maintain their strength. Before patients begin to exercise, however, it may be necessary to perform testing to determine their exercise tolerance. Based on these results, a customized exercise regimen can be developed to match the individual's needs and capabilities. This regimen often includes submaximal aerobic exercise.
There are also specific resistance exercises, such as inspiratory muscle training, that may strengthen the diaphragm muscles. In addition, occupational therapy may help late-onset patients learn new ways to complete daily tasks and job duties.
